CFTR
CFTR,即囊性纖維化跨膜傳導(dǎo)調(diào)節(jié)器,是一種廣泛表達在上皮細胞膜上的ATP門控離子通道,屬于ATP結(jié)合盒式轉(zhuǎn)運體超家族。CFTR的作用機制涉及到兩個核苷酸結(jié)合結(jié)構(gòu)域(NBDs)的二聚化,以及隨后的構(gòu)象變化,這些變化受ATP水解的支配,從而調(diào)節(jié)氯離子的傳導(dǎo)。CFTR的功能異常會導(dǎo)致囊性纖維化,這是一種常見的遺傳性疾病,其特征是體內(nèi)多個組織器官的水鹽平衡失調(diào),引起營養(yǎng)不良、肝臟疾病、反復(fù)的細菌感染、慢性炎癥及呼吸衰竭等癥狀。在生物學(xué)意義上,CFTR對維持上皮細胞膜上的鹽和液體平衡至關(guān)重要,其正常功能對于防止呼吸道和消化道的黏液堵塞、維持肺功能和消化健康具有重要作用。
熱銷產(chǎn)品
Human Cystic fibrosis transmembrane conductance regulator(CFTR) ELISA kit (CSB-EL005292HU)
驗證數(shù)據(jù)

貨號:CSB-EL005292HU
規(guī)格:96T/48T
靈敏度:7 pg/mL
檢測范圍:28 pg/mL-1800 pg/mL
These standard curves are provided for demonstration only. A standard curve should be generated for each set of samples assayed.
CFTR Antibodies
CFTR for Homo sapiens (Human)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 種屬反應(yīng)性 | 應(yīng)用類型 |
---|---|---|---|
CSB-PA001608 | CFTR Antibody | Human,Mouse,Rat | WB, IHC, ELISA |
CSB-PA940971 | CFTR Antibody | Human | ELISA,IHC |
CSB-PA968401 | CFTR Antibody | Human | ELISA,IHC |
CFTR Proteins
CFTR Proteins for Ovis aries (Sheep)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292SH CSB-EP005292SH CSB-BP005292SH CSB-MP005292SH CSB-EP005292SH-B |
Recombinant Sheep Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Oryctolagus cuniculus (Rabbit)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292RB CSB-EP005292RB CSB-BP005292RB CSB-MP005292RB CSB-EP005292RB-B |
Recombinant Rabbit Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Homo sapiens (Human)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292HU CSB-EP005292HU CSB-BP005292HU CSB-MP005292HU CSB-EP005292HU-B |
Recombinant Human Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Mus musculus (Mouse)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292MO CSB-EP005292MO CSB-BP005292MO CSB-MP005292MO CSB-EP005292MO-B |
Recombinant Mouse Cystic fibrosis transmembrane conductance regulator (Cftr), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Bos taurus (Bovine)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292BO CSB-EP005292BO CSB-BP005292BO CSB-MP005292BO CSB-EP005292BO-B |
Recombinant Bovine Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Rattus norvegicus (Rat)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292RA CSB-EP005292RA CSB-BP005292RA CSB-MP005292RA CSB-EP005292RA-B |
Recombinant Rat Cystic fibrosis transmembrane conductance regulator (Cftr), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Squalus acanthias (Spiny dogfish)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292FKW CSB-EP005292FKW CSB-BP005292FKW CSB-MP005292FKW CSB-EP005292FKW-B |
Recombinant Squalus acanthias Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Xenopus laevis (African clawed frog)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP005292XBE CSB-EP005292XBE CSB-BP005292XBE CSB-MP005292XBE CSB-EP005292XBE-B |
Recombinant Xenopus laevis Cystic fibrosis transmembrane conductance regulator (cftr), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Loxodonta africana (African elephant)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP608845LJC CSB-EP608845LJC CSB-BP608845LJC CSB-MP608845LJC CSB-EP608845LJC-B |
Recombinant Loxodonta africana Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Chlorocebus aethiops (Green monkey) (Cercopithecus aethiops)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP639482DSU CSB-EP639482DSU CSB-BP639482DSU CSB-MP639482DSU CSB-EP639482DSU-B |
Recombinant Chlorocebus aethiops Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Gorilla gorilla gorilla (Lowland gorilla)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP639486GGZ CSB-EP639486GGZ CSB-BP639486GGZ CSB-MP639486GGZ CSB-EP639486GGZ-B |
Recombinant Gorilla gorilla gorilla Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Pongo abelii (Sumatran orangutan)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP643184PYX CSB-EP643184PYX CSB-BP643184PYX CSB-MP643184PYX CSB-EP643184PYX-B |
Recombinant Pongo abelii Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Rhinolophus ferrumequinum (Greater horseshoe bat)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP645341RKD CSB-EP645341RKD CSB-BP645341RKD CSB-MP645341RKD CSB-EP645341RKD-B |
Recombinant Rhinolophus ferrumequinum Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Equus caballus (Horse)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP646912HO CSB-EP646912HO CSB-BP646912HO CSB-MP646912HO CSB-EP646912HO-B |
Recombinant Horse Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Otolemur garnettii (Small-eared galago) (Garnett's greater bushbaby)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP646918OFS CSB-EP646918OFS CSB-BP646918OFS CSB-MP646918OFS CSB-EP646918OFS-B |
Recombinant Otolemur garnettii Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Callicebus moloch (Dusky titi monkey)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP649286CYE CSB-EP649286CYE CSB-BP649286CYE CSB-MP649286CYE CSB-EP649286CYE-B |
Recombinant Callicebus moloch Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Microcebus murinus (Lesser mouse lemur)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP650066MFU CSB-EP650066MFU CSB-BP650066MFU CSB-MP650066MFU CSB-EP650066MFU-B |
Recombinant Microcebus murinus Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Carollia perspicillata (Seba's short-tailed bat)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP650849CCAH CSB-EP650849CCAH CSB-BP650849CCAH CSB-MP650849CCAH CSB-EP650849CCAH-B |
Recombinant Carollia perspicillata Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Pan troglodytes (Chimpanzee)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP650850EQV CSB-EP650850EQV CSB-BP650850EQV CSB-MP650850EQV CSB-EP650850EQV-B |
Recombinant Pan troglodytes Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Callithrix jacchus (White-tufted-ear marmoset)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP650851CYL CSB-EP650851CYL CSB-BP650851CYL CSB-MP650851CYL CSB-EP650851CYL-B |
Recombinant Callithrix jacchus Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Didelphis marsupialis virginiana (North American opossum)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP651627DKL CSB-EP651627DKL CSB-BP651627DKL CSB-MP651627DKL CSB-EP651627DKL-B |
Recombinant Didelphis marsupialis virginiana Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Trichosurus vulpecula (Brush-tailed possum)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP688569TQG CSB-EP688569TQG CSB-BP688569TQG CSB-MP688569TQG CSB-EP688569TQG-B |
Recombinant Trichosurus vulpecula Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Canis familiaris (Dog) (Canis lupus familiaris)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP736031DO CSB-EP736031DO CSB-BP736031DO CSB-MP736031DO CSB-EP736031DO-B |
Recombinant Dog Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Macaca fuscata fuscata (Japanese macaque)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP748697MMX CSB-EP748697MMX CSB-BP748697MMX CSB-MP748697MMX CSB-EP748697MMX-B |
Recombinant Macaca fuscata fuscata Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Sus scrofa (Pig)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP754284PI CSB-EP754284PI CSB-BP754284PI CSB-MP754284PI CSB-EP754284PI-B |
Recombinant Pig Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Macaca fascicularis (Crab-eating macaque) (Cynomolgus monkey)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP759053MOV CSB-EP759053MOV CSB-BP759053MOV CSB-MP759053MOV CSB-EP759053MOV-B |
Recombinant Macaca fascicularis Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Papio anubis (Olive baboon)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP871315ERI CSB-EP871315ERI CSB-BP871315ERI CSB-MP871315ERI CSB-EP871315ERI-B |
Recombinant Papio anubis Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR Proteins for Macaca nemestrina (Pig-tailed macaque)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP874690MOX CSB-EP874690MOX CSB-BP874690MOX CSB-MP874690MOX CSB-EP874690MOX-B |
Recombinant Macaca nemestrina Cystic fibrosis transmembrane conductance regulator (CFTR), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CFTR ELISA Kit
CFTR ELISA Kit for Homo sapiens (Human)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 樣本類型 | 靈敏度 |
---|---|---|---|
CSB-EL005292HU | Human Cystic fibrosis transmembrane conductance regulator(CFTR) ELISA kit | serum, plasma, tissue homogenates, cell lysates | 7 pg/mL |