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CFTR

CFTR,即囊性纖維化跨膜傳導(dǎo)調(diào)節(jié)器,是一種廣泛表達在上皮細胞膜上的ATP門控離子通道,屬于ATP結(jié)合盒式轉(zhuǎn)運體超家族。CFTR的作用機制涉及到兩個核苷酸結(jié)合結(jié)構(gòu)域(NBDs)的二聚化,以及隨后的構(gòu)象變化,這些變化受ATP水解的支配,從而調(diào)節(jié)氯離子的傳導(dǎo)。CFTR的功能異常會導(dǎo)致囊性纖維化,這是一種常見的遺傳性疾病,其特征是體內(nèi)多個組織器官的水鹽平衡失調(diào),引起營養(yǎng)不良、肝臟疾病、反復(fù)的細菌感染、慢性炎癥及呼吸衰竭等癥狀。在生物學(xué)意義上,CFTR對維持上皮細胞膜上的鹽和液體平衡至關(guān)重要,其正常功能對于防止呼吸道和消化道的黏液堵塞、維持肺功能和消化健康具有重要作用。

熱銷產(chǎn)品

Human Cystic fibrosis transmembrane conductance regulator(CFTR) ELISA kit (CSB-EL005292HU)

驗證數(shù)據(jù)

CSB-EL005292HU 標準曲線

貨號:CSB-EL005292HU

規(guī)格:96T/48T

靈敏度:7 pg/mL

檢測范圍:28 pg/mL-1800 pg/mL

These standard curves are provided for demonstration only. A standard curve should be generated for each set of samples assayed.

CFTR Antibodies

CFTR for Homo sapiens (Human)

CFTR Proteins

CFTR Proteins for Ovis aries (Sheep)

CFTR Proteins for Oryctolagus cuniculus (Rabbit)

CFTR Proteins for Homo sapiens (Human)

CFTR Proteins for Mus musculus (Mouse)

CFTR Proteins for Bos taurus (Bovine)

CFTR Proteins for Rattus norvegicus (Rat)

CFTR Proteins for Squalus acanthias (Spiny dogfish)

CFTR Proteins for Xenopus laevis (African clawed frog)

CFTR Proteins for Loxodonta africana (African elephant)

CFTR Proteins for Chlorocebus aethiops (Green monkey) (Cercopithecus aethiops)

CFTR Proteins for Gorilla gorilla gorilla (Lowland gorilla)

CFTR Proteins for Pongo abelii (Sumatran orangutan)

CFTR Proteins for Rhinolophus ferrumequinum (Greater horseshoe bat)

CFTR Proteins for Equus caballus (Horse)

CFTR Proteins for Otolemur garnettii (Small-eared galago) (Garnett's greater bushbaby)

CFTR Proteins for Callicebus moloch (Dusky titi monkey)

CFTR Proteins for Microcebus murinus (Lesser mouse lemur)

CFTR Proteins for Carollia perspicillata (Seba's short-tailed bat)

CFTR Proteins for Pan troglodytes (Chimpanzee)

CFTR Proteins for Callithrix jacchus (White-tufted-ear marmoset)

CFTR Proteins for Didelphis marsupialis virginiana (North American opossum)

CFTR Proteins for Trichosurus vulpecula (Brush-tailed possum)

CFTR Proteins for Canis familiaris (Dog) (Canis lupus familiaris)

CFTR Proteins for Macaca fuscata fuscata (Japanese macaque)

CFTR Proteins for Sus scrofa (Pig)

CFTR Proteins for Macaca fascicularis (Crab-eating macaque) (Cynomolgus monkey)

CFTR Proteins for Papio anubis (Olive baboon)

CFTR Proteins for Macaca nemestrina (Pig-tailed macaque)

CFTR ELISA Kit

CFTR ELISA Kit for Homo sapiens (Human)