TCAP
TCAP,別名Telethonin、T-cap、LGMD2G、LGMDR7等,是一種由人類TCAP基因編碼的蛋白質(zhì),主要在橫紋肌和心肌中表達(dá),與肌肉的結(jié)構(gòu)和功能密切相關(guān)。
TCAP可以與肌聯(lián)蛋白的Z1-Z2結(jié)構(gòu)域結(jié)合,作為肌聯(lián)蛋白激酶的底物,對(duì)肌節(jié)組裝至關(guān)重要。TCAP基因的突變與四肢帶型肌營(yíng)養(yǎng)不良2G(LGMD2G)和心肌病有關(guān)。TCAP在維持肌肉結(jié)構(gòu)完整性和功能中發(fā)揮重要作用,其異常表達(dá)或功能喪失可能導(dǎo)致肌肉疾病,包括肌營(yíng)養(yǎng)不良和心肌癥。
熱銷產(chǎn)品
Recombinant Human Telethonin (TCAP) (CSB-EP023264HU)
驗(yàn)證數(shù)據(jù)

(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.
TCAP Antibody (CSB-PA023264ESR1HU)
驗(yàn)證數(shù)據(jù)

Immunohistochemistry of paraffin-embedded human skeletal muscle tissue using CSB-PA023264ESR1HU at dilution of 1:100

Immunohistochemistry of paraffin-embedded human heart tissue using CSB-PA023264ESR1HU at dilution of 1:100
TCAP Antibodies
TCAP for Homo sapiens (Human)
產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 種屬反應(yīng)性 | 應(yīng)用類型 |
---|---|---|---|
CSB-PA023264ESR1HU | TCAP Antibody | Human | ELISA, IHC |
TCAP Proteins
TCAP Proteins for Homo sapiens (Human)
產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-YP023264HU CSB-BP023264HU CSB-MP023264HU CSB-EP023264HU-B |
Recombinant Human Telethonin (TCAP) | Yeast Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CSB-EP023264HU | Recombinant Human Telethonin (TCAP) | E.coli |