EARS2 Antibody
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中文名稱:EARS2兔多克隆抗體
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貨號(hào):CSB-PA705509LA01HU
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規(guī)格:¥440
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圖片:
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其他:
產(chǎn)品詳情
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產(chǎn)品名稱:Rabbit anti-Homo sapiens (Human) EARS2 Polyclonal antibody
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Uniprot No.:
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基因名:EARS2
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別名:3230401I01Rik antibody; AL024049 antibody; COXPD12 antibody; EARS 2 antibody; ears2 antibody; GluRS antibody; Glutamate--tRNA ligase antibody; Glutamyl tRNA synthetase 2 mitochondrial antibody; KIAA1970 antibody; mitochondrial antibody; mKIAA1970 antibody; MSE1 antibody; Probable glutamyl tRNA synthetase; mitochondrial antibody; Probable glutamyl-tRNA synthetase antibody; RGD1307904 antibody; SYEM_HUMAN antibody
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宿主:Rabbit
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反應(yīng)種屬:Human
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免疫原:Recombinant Human Probable glutamate--tRNA ligase, mitochondrial protein (42-166AA)
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免疫原種屬:Homo sapiens (Human)
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標(biāo)記方式:Non-conjugated
本頁面中的產(chǎn)品,EARS2 Antibody (CSB-PA705509LA01HU),的標(biāo)記方式是Non-conjugated。對(duì)于EARS2 Antibody,我們還提供其他標(biāo)記。見下表:
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克隆類型:Polyclonal
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抗體亞型:IgG
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純化方式:>95%, Protein G purified
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濃度:It differs from different batches. Please contact us to confirm it.
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保存緩沖液:Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, pH 7.4 -
產(chǎn)品提供形式:Liquid
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應(yīng)用范圍:ELISA, IHC
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推薦稀釋比:
Application Recommended Dilution IHC 1:20-1:200 -
Protocols:
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儲(chǔ)存條件:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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貨期:Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
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用途:For Research Use Only. Not for use in diagnostic or therapeutic procedures.
引用文獻(xiàn)
- B cell dysfunction in thalamus and brainstem involvement and high lactate caused by novel mutation of EARS2 gene Y Wen, Y Huang, W Zhang, P Chen, X Hu, X Xiong,Italian Journal of Pediatrics,2025
相關(guān)產(chǎn)品
靶點(diǎn)詳情
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功能:Catalyzes the attachment of glutamate to tRNA(Glu) in a two-step reaction: glutamate is first activated by ATP to form Glu-AMP and then transferred to the acceptor end of tRNA(Glu).
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基因功能參考文獻(xiàn):
- This study presented that a new neurological disease, early-onset leukoencephalopathy with thalamus and brainstem involvement and high lactate, defined by a peculiar biphasic clinical course and caused by mutations in a single gene, EARS2. PMID: 22492562
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相關(guān)疾?。?/div>Combined oxidative phosphorylation deficiency 12 (COXPD12)亞細(xì)胞定位:Mitochondrion matrix.蛋白家族:Class-I aminoacyl-tRNA synthetase family, Glutamate--tRNA ligase type 1 subfamily數(shù)據(jù)庫鏈接:
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