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世界血友病日

世界血友病日

每年的4月17日是世界血友病日,由世界血友病聯(lián)盟發(fā)起,自1989年起設(shè)立,旨在紀念血友病防治事業(yè)的先驅(qū)——加拿大籍的法蘭克?舒納波先生,并喚起全球?qū)ρ巡』颊叩年P(guān)注與支持。

血友病是一種遺傳性出血性疾病,因凝血因子缺乏導(dǎo)致凝血功能障礙,患者常表現(xiàn)為輕微磕碰后血流不止、血腫形成,甚至關(guān)節(jié)出血致殘,嚴重時顱內(nèi)出血或內(nèi)臟出血可能危及生命。根據(jù)凝血因子缺乏的類型,血友病可分為A型(占80%-85%)、B型(占15%-20%)和C型(極少數(shù))。作為一種X染色體連鎖隱性遺傳病,男性發(fā)病,女性傳遞。

血友病的嚴重性和不可預(yù)測性對患者的生活帶來了巨大挑戰(zhàn)。一次輕微的磕碰可能引發(fā)血流不止,甚至一次嚴重的關(guān)節(jié)出血就足以致殘,而顱內(nèi)或內(nèi)臟出血可能在短時間內(nèi)致命。面對這樣的疾病,科學(xué)的治療和管理方案顯得尤為重要。

華美生物致力于為科研人員提供高質(zhì)量的生物試劑,特別整理了血友病研究相關(guān)的重組蛋白、抗體和ELISA試劑盒等產(chǎn)品,旨在助力科研人員深入探索疾病機制,加速診療方案開發(fā)。

血友病研究熱門靶點:

血友病研究相關(guān)產(chǎn)品推薦:

● 重組蛋白:

產(chǎn)品名稱 貨號 靶點 來源 蛋白標(biāo)簽
Recombinant Mouse Serum albumin (Alb) CSB-BP001561MO Alb Baculovirus C-terminal 9xHis-tagged
Recombinant Marmota monax Tumor necrosis factor (TNF), partial CSB-BP523593MQG TNF Baculovirus N-terminal 10xHis-tagged
Recombinant Human T-cell surface glycoprotein CD4 (CD4), partial CSB-CF004935HU1 CD4 in vitro E.coli expression system N-terminal 6xHis-tagged
Recombinant Dog Serum albumin (ALB) CSB-EP001561DO ALB E.coli N-terminal 6xHis-tagged
Recombinant Macaca fascicularis albumin (ALB) CSB-EP001561MOV ALB E.coli N-terminal 6xHis-SUMO-tagged
Recombinant Human Coagulation factor XI (F11), partial CSB-EP007916HU F11 E.coli N-terminal 6xHis-tagged
Recombinant Pig Coagulation factor XII (F12), partial CSB-EP007918PI F12 E.coli N-terminal 6xHis-tagged
Recombinant Human Prothrombin (F2) CSB-EP007923HU F2 E.coli N-terminal 6xHis-SUMO-tagged
Recombinant Human Tissue factor (F3), partial CSB-EP007928HU1 F3 E.coli N-terminal 6xHis-SUMO-tagged
Recombinant Human Coagulation factor V (F5), partial CSB-EP007929HU F5 E.coli N-terminal 6xHis-SUMO-tagged
Recombinant Human Coagulation factor VII (F7), partial CSB-EP007930HU F7 E.coli N-terminal 6xHis-SUMO-tagged
Recombinant Human Fibrinogen beta chain (FGB), partial CSB-EP008608HU FGB E.coli N-terminal 6xHis-tagged
Recombinant Chicken Interferon gamma (IFNG) CSB-EP011050CH IFNG E.coli N-terminal GST-tagged
Recombinant Human Interferon gamma (IFNG) CSB-EP011050HU IFNG E.coli N-terminal 6xHis-tagged
Recombinant Mouse Interferon gamma (Ifng), partial CSB-EP011050MO1 Ifng E.coli N-terminal 6xHis-tagged
Recombinant Marmota monax Interferon gamma (IFNG) CSB-EP011050MQG IFNG E.coli N-terminal 6xHis-tagged
Recombinant Rat Interferon gamma (Ifng) CSB-EP011050RA Ifng E.coli N-terminal GST-tagged
Recombinant Sheep Interferon gamma (IFNG) CSB-EP011050SH IFNG E.coli N-terminal 6xHis-tagged
Recombinant Bovie Tumor necrosis factor (TNF), partial CSB-EP023955BO TNF E.coli N-terminal 6xHis-tagged
Recombinant Bovie Tumor necrosis factor (TNF), partial CSB-EP023955BOe0 TNF E.coli N-terminal GST-tagged

● 抗體:

CSB-RA599469A0HU IHC

F10 Recombinant Monoclonal Antibody
CSB-RA599469A0HU

Tested Applications: ELISA, IHC

CSB-RA912740A0HU IHC

F2 Recombinant Monoclonal Antibody
CSB-RA912740A0HU

Tested Applications: ELISA, IHC

CSB-RA776663A0HU WB

F3 Recombinant Monoclonal Antibody
CSB-RA776663A0HU

Tested Applications: ELISA, WB, IHC

CSB-RA923075A0HU WB

F9 Recombinant Monoclonal Antibody
CSB-RA923075A0HU

Tested Applications: ELISA, WB

- 重組抗體

靶點 產(chǎn)品名稱 貨號 反應(yīng)種屬 應(yīng)用范圍
ALB ALB Recombinant Monoclonal Antibody CSB-RA264109A0HU Human ELISA, FC
CD4 CD4 Recombinant Monoclonal Antibody CSB-RA004935A0HU Human ELISA, WB, IHC
CRP CRP Recombinant Monoclonal Antibody CSB-RA988767A0HU Human ELISA, IHC
F10 F10 Recombinant Monoclonal Antibody CSB-RA599469A0HU Human ELISA, IHC
F2 F2 Recombinant Monoclonal Antibody CSB-RA912740A0HU Human ELISA, IHC
F3 F3 Recombinant Monoclonal Antibody CSB-RA776663A0HU Human, Rat ELISA, WB, IHC
F9 F9 Recombinant Monoclonal Antibody CSB-RA923075A0HU Human ELISA, WB

- 單克隆抗體:

靶點 產(chǎn)品名稱 貨號 反應(yīng)種屬 應(yīng)用范圍
ALB ALB Monoclonal Antibody CSB-MA076752 Human ELISA, WB, IHC
CD4 CD4 Monoclonal Antibody CSB-MA000228 Human,Mouse,Rat ELISA, IHC
CD4 CD4 Monoclonal Antibody,APC Conjugated CSB-MA043428 Human ELISA, IF, FC
CD4 CD4 Monoclonal Antibody,Biotin Conjugated CSB-MA981329 Human ELISA, IF, FC
CD4 CD4 Monoclonal Antibody,FITC Conjugated CSB-MA124048 Human ELISA, IF, FC
CD4 CD4 Monoclonal Antibody,PE Conjugated CSB-MA260243 Human ELISA, IF, FC
CD4 CD4 Monoclonal Antibody,PE-Cy5 Conjugated CSB-MA570802 Human ELISA, IF, FC
CD4 CD4 Monoclonal Antibody,Purified CSB-MA783233 Human ELISA, FC
CD4 CD4 Monoclonal Antibody,PE Conjugated CSB-MA084552 Mouse ELISA, FC
CRP CRP Monoclonal Antibody CSB-MA027411E0m Human ELISA, IHC
F13A1 F13A1 Monoclonal Antibody CSB-MA177758 Human ELISA, IHC
IFNG IFNG Monoclonal Antibody CSB-MA065241A0m Human ELISA, IHC
TNF TNF Monoclonal Antibody CSB-MA084771A0m Bovine ELISA
TNF TNF Monoclonal Antibody CSB-MA080271 Human,Mouse,Rat ELISA, WB, IHC
TNF TNF Monoclonal Antibody CSB-MA080272 Human,Mouse,Rat ELISA, WB, IHC

- 多克隆抗體:

產(chǎn)品名稱 貨號 靶點 反應(yīng)種屬 應(yīng)用范圍
ALB Antibody CSB-PA00260E1Rb ALB Canine ELISA
ALB Antibody, HRP conjugated CSB-PA00260F1Rb ALB Canine ELISA
ALB Antibody, FITC conjugated CSB-PA00260G1Rb ALB Canine
ALB Antibody, Biotin conjugated CSB-PA00260H1Rb ALB Canine ELISA
ALB Antibody CSB-PA00950E1Rb ALB Bovine ELISA
ALB Antibody, HRP conjugated CSB-PA00950F1Rb ALB Bovine ELISA
ALB Antibody, FITC conjugated CSB-PA00950G1Rb ALB Bovine
ALB Antibody, Biotin conjugated CSB-PA00950H1Rb ALB Bovine ELISA
ALB Antibody CSB-PA001561LA01HU ALB Human, Mouse ELISA, WB, IHC, IF
ALB Antibody, HRP conjugated CSB-PA001561LB01HU ALB Human ELISA
ALB Antibody, FITC conjugated CSB-PA001561LC01HU ALB Human
ALB Antibody, Biotin conjugated CSB-PA001561LD01HU ALB Human ELISA
Alb Antibody CSB-PA001561LA01RA Alb Rat ELISA, WB
Alb Antibody, HRP conjugated CSB-PA001561LB01RA Alb Rat ELISA
Alb Antibody, FITC conjugated CSB-PA001561LC01RA Alb Rat
Alb Antibody, Biotin conjugated CSB-PA001561LD01RA Alb Rat ELISA
ALB Antibody CSB-PA001561GA01HU ALB Human, Mouse, Rat ELISA, IHC
ALB Antibody CSB-PA079344 ALB Human ELISA, WB, IHC
BSA Antibody CSB-PA592874 ALB Bovine ELISA, WB
BSA Antibody CSB-PA272395 ALB Bovine ELISA, WB

● ELISA試劑盒:

產(chǎn)品名稱 貨號 靶點 樣本類型 檢測范圍
犬白蛋白(Alb)酶聯(lián)免疫試劑盒 CSB-E15757c ALB serum, plasma, tissue homogenates 0.273 μg/mL-35 μg/mL
小鼠白蛋白酶聯(lián)免疫試劑盒 CSB-E13878m ALB serum, plasma, tissue homogenates 0.781 μg/mL-200 μg/mL
豬白蛋白酶聯(lián)免疫試劑盒 CSB-E16207p ALB serum, plasma, urine 0.03 μg/mL-7000 μg/mL
豬腫瘤壞死因子alpha(TNF/TNFA/TNFSF2)酶聯(lián)免疫試劑盒 CSB-E16980p TNF serum, plasma, cell culture supernates, tissue homogenates 0.047 ng/mL-3 ng/mL
人血管性血友病因子/瑞斯托霉素輔因子(VWF)酶聯(lián)免疫試劑盒 CSB-E08437h VWF serum, plasma, tissue homogenates. 6.25 ng/ml-400 ng/ml.
綿羊白蛋白酶聯(lián)免疫試劑盒 CSB-E15839Sh ALB serum, plasma, cell culture supernates, urine, tissue homogenates 5.47 μg/ml-350 μg/ml
大鼠凝血因子ⅩⅢ(FⅩⅢ)酶聯(lián)免疫試劑盒 CSB-E10122r F13A1
馬白蛋白酶聯(lián)免疫試劑盒 CSB-E16205Hs ALB serum, plasma 1.25 μg/mL-80 μg/mL
牛白蛋白(ALB)酶聯(lián)免疫試劑盒 CSB-E08664b ALB serum, plasma, tissue homogenates 0.313 μg/mL-80 μg/mL
豬腫瘤壞死因子alpha(TNF/TNFA/TNFSF2)酶聯(lián)免疫試劑盒 CSB-E16980p-IS TNF serum, plasma, cell culture supernates, tissue homogenates 23.5 pg/mL-1500 pg/mL
大鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 CSB-E04579r-IS IFNG serum, plasma, cell culture supernates, tissue homogenates 31.25 pg/mL-2000 pg/mL
豬γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 CSB-E06794p-IS IFNG serum, plasma, tissue homogenates 6.25 pg/mL-400 pg/mL
小鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 CSB-E04578m-IS IFNG
大鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 CSB-E11987r-IS TNF tissue homogenates, cell culture supernates, bronchoalveolar lavage fluid 15.6 pg/mL-1000 pg/mL
小鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 CSB-E04741m(1) TNF cell culture supernates, tissue homogenates 62.5 pg/mL-4000 pg/mL
小鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 CSB-E04578m(1) IFNG serum, plasma, tissue homogenates 0.156 ng/mL-10 ng/mL
小鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 CSB-E04741m-IS TNF serum, plasma, tissue homogenates, cell culture supernates 7.8 pg/ml-500 pg/ml
人腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 CSB-E04740h-IS TNF cell culture supernates 7.8 pg/mL-500 pg/mL
山羊白蛋白(Alb)酶聯(lián)免疫試劑盒 CSB-E15758G ALB serum, plasma, tissue homogenates 0.17 μg/mL-350 μg/mL
兔白蛋白酶聯(lián)免疫試劑盒 CSB-E16204Rb ALB serum, plasma, urine 0.273 μg/mL-70 μg/mL