
每年的4月17日是世界血友病日,由世界血友病聯(lián)盟發(fā)起,自1989年起設(shè)立,旨在紀念血友病防治事業(yè)的先驅(qū)——加拿大籍的法蘭克?舒納波先生,并喚起全球?qū)ρ巡』颊叩年P(guān)注與支持。
血友病是一種遺傳性出血性疾病,因凝血因子缺乏導(dǎo)致凝血功能障礙,患者常表現(xiàn)為輕微磕碰后血流不止、血腫形成,甚至關(guān)節(jié)出血致殘,嚴重時顱內(nèi)出血或內(nèi)臟出血可能危及生命。根據(jù)凝血因子缺乏的類型,血友病可分為A型(占80%-85%)、B型(占15%-20%)和C型(極少數(shù))。作為一種X染色體連鎖隱性遺傳病,男性發(fā)病,女性傳遞。
血友病的嚴重性和不可預(yù)測性對患者的生活帶來了巨大挑戰(zhàn)。一次輕微的磕碰可能引發(fā)血流不止,甚至一次嚴重的關(guān)節(jié)出血就足以致殘,而顱內(nèi)或內(nèi)臟出血可能在短時間內(nèi)致命。面對這樣的疾病,科學(xué)的治療和管理方案顯得尤為重要。
華美生物致力于為科研人員提供高質(zhì)量的生物試劑,特別整理了血友病研究相關(guān)的重組蛋白、抗體和ELISA試劑盒等產(chǎn)品,旨在助力科研人員深入探索疾病機制,加速診療方案開發(fā)。
血友病研究熱門靶點:
血友病研究相關(guān)產(chǎn)品推薦:
● 重組蛋白:
產(chǎn)品名稱 | 貨號 | 靶點 | 來源 | 蛋白標(biāo)簽 |
---|---|---|---|---|
Recombinant Mouse Serum albumin (Alb) | CSB-BP001561MO | Alb | Baculovirus | C-terminal 9xHis-tagged |
Recombinant Marmota monax Tumor necrosis factor (TNF), partial | CSB-BP523593MQG | TNF | Baculovirus | N-terminal 10xHis-tagged |
Recombinant Human T-cell surface glycoprotein CD4 (CD4), partial | CSB-CF004935HU1 | CD4 | in vitro E.coli expression system | N-terminal 6xHis-tagged |
Recombinant Dog Serum albumin (ALB) | CSB-EP001561DO | ALB | E.coli | N-terminal 6xHis-tagged |
Recombinant Macaca fascicularis albumin (ALB) | CSB-EP001561MOV | ALB | E.coli | N-terminal 6xHis-SUMO-tagged |
Recombinant Human Coagulation factor XI (F11), partial | CSB-EP007916HU | F11 | E.coli | N-terminal 6xHis-tagged |
Recombinant Pig Coagulation factor XII (F12), partial | CSB-EP007918PI | F12 | E.coli | N-terminal 6xHis-tagged |
Recombinant Human Prothrombin (F2) | CSB-EP007923HU | F2 | E.coli | N-terminal 6xHis-SUMO-tagged |
Recombinant Human Tissue factor (F3), partial | CSB-EP007928HU1 | F3 | E.coli | N-terminal 6xHis-SUMO-tagged |
Recombinant Human Coagulation factor V (F5), partial | CSB-EP007929HU | F5 | E.coli | N-terminal 6xHis-SUMO-tagged |
Recombinant Human Coagulation factor VII (F7), partial | CSB-EP007930HU | F7 | E.coli | N-terminal 6xHis-SUMO-tagged |
Recombinant Human Fibrinogen beta chain (FGB), partial | CSB-EP008608HU | FGB | E.coli | N-terminal 6xHis-tagged |
Recombinant Chicken Interferon gamma (IFNG) | CSB-EP011050CH | IFNG | E.coli | N-terminal GST-tagged |
Recombinant Human Interferon gamma (IFNG) | CSB-EP011050HU | IFNG | E.coli | N-terminal 6xHis-tagged |
Recombinant Mouse Interferon gamma (Ifng), partial | CSB-EP011050MO1 | Ifng | E.coli | N-terminal 6xHis-tagged |
Recombinant Marmota monax Interferon gamma (IFNG) | CSB-EP011050MQG | IFNG | E.coli | N-terminal 6xHis-tagged |
Recombinant Rat Interferon gamma (Ifng) | CSB-EP011050RA | Ifng | E.coli | N-terminal GST-tagged |
Recombinant Sheep Interferon gamma (IFNG) | CSB-EP011050SH | IFNG | E.coli | N-terminal 6xHis-tagged |
Recombinant Bovie Tumor necrosis factor (TNF), partial | CSB-EP023955BO | TNF | E.coli | N-terminal 6xHis-tagged |
Recombinant Bovie Tumor necrosis factor (TNF), partial | CSB-EP023955BOe0 | TNF | E.coli | N-terminal GST-tagged |
● 抗體:
- 重組抗體
靶點 | 產(chǎn)品名稱 | 貨號 | 反應(yīng)種屬 | 應(yīng)用范圍 |
ALB | ALB Recombinant Monoclonal Antibody | CSB-RA264109A0HU | Human | ELISA, FC |
CD4 | CD4 Recombinant Monoclonal Antibody | CSB-RA004935A0HU | Human | ELISA, WB, IHC |
CRP | CRP Recombinant Monoclonal Antibody | CSB-RA988767A0HU | Human | ELISA, IHC |
F10 | F10 Recombinant Monoclonal Antibody | CSB-RA599469A0HU | Human | ELISA, IHC |
F2 | F2 Recombinant Monoclonal Antibody | CSB-RA912740A0HU | Human | ELISA, IHC |
F3 | F3 Recombinant Monoclonal Antibody | CSB-RA776663A0HU | Human, Rat | ELISA, WB, IHC |
F9 | F9 Recombinant Monoclonal Antibody | CSB-RA923075A0HU | Human | ELISA, WB |
- 單克隆抗體:
靶點 | 產(chǎn)品名稱 | 貨號 | 反應(yīng)種屬 | 應(yīng)用范圍 |
ALB | ALB Monoclonal Antibody | CSB-MA076752 | Human | ELISA, WB, IHC |
CD4 | CD4 Monoclonal Antibody | CSB-MA000228 | Human,Mouse,Rat | ELISA, IHC |
CD4 | CD4 Monoclonal Antibody,APC Conjugated | CSB-MA043428 | Human | ELISA, IF, FC |
CD4 | CD4 Monoclonal Antibody,Biotin Conjugated | CSB-MA981329 | Human | ELISA, IF, FC |
CD4 | CD4 Monoclonal Antibody,FITC Conjugated | CSB-MA124048 | Human | ELISA, IF, FC |
CD4 | CD4 Monoclonal Antibody,PE Conjugated | CSB-MA260243 | Human | ELISA, IF, FC |
CD4 | CD4 Monoclonal Antibody,PE-Cy5 Conjugated | CSB-MA570802 | Human | ELISA, IF, FC |
CD4 | CD4 Monoclonal Antibody,Purified | CSB-MA783233 | Human | ELISA, FC |
CD4 | CD4 Monoclonal Antibody,PE Conjugated | CSB-MA084552 | Mouse | ELISA, FC |
CRP | CRP Monoclonal Antibody | CSB-MA027411E0m | Human | ELISA, IHC |
F13A1 | F13A1 Monoclonal Antibody | CSB-MA177758 | Human | ELISA, IHC |
IFNG | IFNG Monoclonal Antibody | CSB-MA065241A0m | Human | ELISA, IHC |
TNF | TNF Monoclonal Antibody | CSB-MA084771A0m | Bovine | ELISA |
TNF | TNF Monoclonal Antibody | CSB-MA080271 | Human,Mouse,Rat | ELISA, WB, IHC |
TNF | TNF Monoclonal Antibody | CSB-MA080272 | Human,Mouse,Rat | ELISA, WB, IHC |
- 多克隆抗體:
產(chǎn)品名稱 | 貨號 | 靶點 | 反應(yīng)種屬 | 應(yīng)用范圍 |
---|---|---|---|---|
ALB Antibody | CSB-PA00260E1Rb | ALB | Canine | ELISA |
ALB Antibody, HRP conjugated | CSB-PA00260F1Rb | ALB | Canine | ELISA |
ALB Antibody, FITC conjugated | CSB-PA00260G1Rb | ALB | Canine | |
ALB Antibody, Biotin conjugated | CSB-PA00260H1Rb | ALB | Canine | ELISA |
ALB Antibody | CSB-PA00950E1Rb | ALB | Bovine | ELISA |
ALB Antibody, HRP conjugated | CSB-PA00950F1Rb | ALB | Bovine | ELISA |
ALB Antibody, FITC conjugated | CSB-PA00950G1Rb | ALB | Bovine | |
ALB Antibody, Biotin conjugated | CSB-PA00950H1Rb | ALB | Bovine | ELISA |
ALB Antibody | CSB-PA001561LA01HU | ALB | Human, Mouse | ELISA, WB, IHC, IF |
ALB Antibody, HRP conjugated | CSB-PA001561LB01HU | ALB | Human | ELISA |
ALB Antibody, FITC conjugated | CSB-PA001561LC01HU | ALB | Human | |
ALB Antibody, Biotin conjugated | CSB-PA001561LD01HU | ALB | Human | ELISA |
Alb Antibody | CSB-PA001561LA01RA | Alb | Rat | ELISA, WB |
Alb Antibody, HRP conjugated | CSB-PA001561LB01RA | Alb | Rat | ELISA |
Alb Antibody, FITC conjugated | CSB-PA001561LC01RA | Alb | Rat | |
Alb Antibody, Biotin conjugated | CSB-PA001561LD01RA | Alb | Rat | ELISA |
ALB Antibody | CSB-PA001561GA01HU | ALB | Human, Mouse, Rat | ELISA, IHC |
ALB Antibody | CSB-PA079344 | ALB | Human | ELISA, WB, IHC |
BSA Antibody | CSB-PA592874 | ALB | Bovine | ELISA, WB |
BSA Antibody | CSB-PA272395 | ALB | Bovine | ELISA, WB |
● ELISA試劑盒:

Human Antithrombin III(AT III)ELISA Kit
CSB-E17902h

Human coagulation factor Ⅹ,FⅩ ELISA Kit
CSB-E08440h

Human Coagulation factor XI(F11) ELISA kit
CSB-EL007916HU
產(chǎn)品名稱 | 貨號 | 靶點 | 樣本類型 | 檢測范圍 |
---|---|---|---|---|
犬白蛋白(Alb)酶聯(lián)免疫試劑盒 | CSB-E15757c | ALB | serum, plasma, tissue homogenates | 0.273 μg/mL-35 μg/mL |
小鼠白蛋白酶聯(lián)免疫試劑盒 | CSB-E13878m | ALB | serum, plasma, tissue homogenates | 0.781 μg/mL-200 μg/mL |
豬白蛋白酶聯(lián)免疫試劑盒 | CSB-E16207p | ALB | serum, plasma, urine | 0.03 μg/mL-7000 μg/mL |
豬腫瘤壞死因子alpha(TNF/TNFA/TNFSF2)酶聯(lián)免疫試劑盒 | CSB-E16980p | TNF | serum, plasma, cell culture supernates, tissue homogenates | 0.047 ng/mL-3 ng/mL |
人血管性血友病因子/瑞斯托霉素輔因子(VWF)酶聯(lián)免疫試劑盒 | CSB-E08437h | VWF | serum, plasma, tissue homogenates. | 6.25 ng/ml-400 ng/ml. |
綿羊白蛋白酶聯(lián)免疫試劑盒 | CSB-E15839Sh | ALB | serum, plasma, cell culture supernates, urine, tissue homogenates | 5.47 μg/ml-350 μg/ml |
大鼠凝血因子ⅩⅢ(FⅩⅢ)酶聯(lián)免疫試劑盒 | CSB-E10122r | F13A1 | ||
馬白蛋白酶聯(lián)免疫試劑盒 | CSB-E16205Hs | ALB | serum, plasma | 1.25 μg/mL-80 μg/mL |
牛白蛋白(ALB)酶聯(lián)免疫試劑盒 | CSB-E08664b | ALB | serum, plasma, tissue homogenates | 0.313 μg/mL-80 μg/mL |
豬腫瘤壞死因子alpha(TNF/TNFA/TNFSF2)酶聯(lián)免疫試劑盒 | CSB-E16980p-IS | TNF | serum, plasma, cell culture supernates, tissue homogenates | 23.5 pg/mL-1500 pg/mL |
大鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 | CSB-E04579r-IS | IFNG | serum, plasma, cell culture supernates, tissue homogenates | 31.25 pg/mL-2000 pg/mL |
豬γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 | CSB-E06794p-IS | IFNG | serum, plasma, tissue homogenates | 6.25 pg/mL-400 pg/mL |
小鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 | CSB-E04578m-IS | IFNG | ||
大鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 | CSB-E11987r-IS | TNF | tissue homogenates, cell culture supernates, bronchoalveolar lavage fluid | 15.6 pg/mL-1000 pg/mL |
小鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 | CSB-E04741m(1) | TNF | cell culture supernates, tissue homogenates | 62.5 pg/mL-4000 pg/mL |
小鼠γ干擾素(IFN-γ)酶聯(lián)免疫試劑盒 | CSB-E04578m(1) | IFNG | serum, plasma, tissue homogenates | 0.156 ng/mL-10 ng/mL |
小鼠腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 | CSB-E04741m-IS | TNF | serum, plasma, tissue homogenates, cell culture supernates | 7.8 pg/ml-500 pg/ml |
人腫瘤壞死因子α(TNF-α)酶聯(lián)免疫試劑盒 | CSB-E04740h-IS | TNF | cell culture supernates | 7.8 pg/mL-500 pg/mL |
山羊白蛋白(Alb)酶聯(lián)免疫試劑盒 | CSB-E15758G | ALB | serum, plasma, tissue homogenates | 0.17 μg/mL-350 μg/mL |
兔白蛋白酶聯(lián)免疫試劑盒 | CSB-E16204Rb | ALB | serum, plasma, urine | 0.273 μg/mL-70 μg/mL |